Arrhythmogenic noncompaction cardiomyopathy: Is there an echocardiographic phenotypic overlap of two distinct cardiomyopathies?
Journal of Cardiovascular Ultrasound, cilt.23, sa.3, ss.186-190, 2015 (Scopus)
- Yayın Türü: Makale / Tam Makale
- Cilt numarası: 23 Sayı: 3
- Basım Tarihi: 2015
- Doi Numarası: 10.4250/jcu.2015.23.3.186
- Dergi Adı: Journal of Cardiovascular Ultrasound
- Derginin Tarandığı İndeksler: Scopus
- Sayfa Sayıları: ss.186-190
- Anahtar Kelimeler: Arrhythmogenic cardiomyopathy, Noncompaction cardiomyopathy
- Sağlık Bilimleri Üniversitesi Adresli: Evet
Özet
The clinical diagnosis of right ventricular (RV) cardiomyopathies is often challenging. It is difficult to differentiate the isolated left ventricular (LV) noncompaction cardiomyopathy (NC) from biventricular NC or from coexisting arrhythmogenic ventricular cardiomyopathy (AC). There are currently few established morphologic criteria for the diagnosis other than RV dilation and presence of excessive regional trabeculation. The gross and microscopic changes suggest pathological similarities between, or coexistence of, RV-NC and AC. Therefore, the term arrhythmogenic right ventricular cardiomyopathy is somewhat misleading as isolated LV or biventricular involvement may be present and thus a broader term such as AC should be preferred. We describe an unusual case of AC associated with a NC in a 27-year-old man who had a history of permanent pacemaker 7 years ago due to second-degree atrioventricular block.