Intestinal lymphangiectasia unresponsive to classical therapy Klasik tedaviye yanitsiz intestinal lenfanjiyektazi
Turkiye Klinikleri Pediatri, cilt.29, sa.2, ss.119-123, 2020 (Scopus, TRDizin)
- Yayın Türü: Makale / Tam Makale
- Cilt numarası: 29 Sayı: 2
- Basım Tarihi: 2020
- Doi Numarası: 10.5336/pediatr.2020-74568
- Dergi Adı: Turkiye Klinikleri Pediatri
- Derginin Tarandığı İndeksler: Scopus, Academic Search Premier, EMBASE, TR DİZİN (ULAKBİM)
- Sayfa Sayıları: ss.119-123
- Anahtar Kelimeler: Child, Primary intestinal lymphangiectasia, Protein-losing enteropathy
- Sağlık Bilimleri Üniversitesi Adresli: Evet
Özet
Intestinal lymphangiectasia (IL) is an important cause of protein-losing enteropathy. It can either be primary or secondary to conditions causing obstruction of intestinal lymphatics. Loss of proteinrich chylous fluid from the intestinal lumen results in hypoproteinemia and hypoalbuminemia. The classical symptoms are bilateral or unilateral lower limb edema and intermittent diarrhea. The management of primary IL includes dietary modification as first-line therapy. Nutritional regulation for protein-rich, medium-chain fat-containing, poorfat diet is the main factor in the treatment of IL. In this article, we present a patient with protein-losing enteropathy, who was diagnosed with primary IL and did not respond to classical therapy.