Arterio-veno-lymphatic vascular malformation presenting as an anterior mediastinal mass
Indian Journal of Pathology and Microbiology, cilt.68, sa.4, ss.803-805, 2025 (SCI-Expanded, Scopus)
- Yayın Türü: Makale / Tam Makale
- Cilt numarası: 68 Sayı: 4
- Basım Tarihi: 2025
- Doi Numarası: 10.4103/ijpm.ijpm_457_24
- Dergi Adı: Indian Journal of Pathology and Microbiology
- Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus, CINAHL, EMBASE, Directory of Open Access Journals
- Sayfa Sayıları: ss.803-805
- Anahtar Kelimeler: Mediastinal lymphatic venous malformation, mediastinal mass, vascular malformations
- Sağlık Bilimleri Üniversitesi Adresli: Evet
Özet
Mediastinal lymphatic venous malformation (LVM) is considered tumor-like vascular dysplasias that are rarely found in the mediastinum. Clinical presentation of LVMs varies depending on the patient. Patients may be asymptomatic or may present with symptoms such as cough, chest pain, dyspnea, and hemoptysis. A 4-year-old girl was admitted to the hospital with complaints of coughing attacks, shortness of breath in the right lateral decubitus position, and restlessness. A contrast-enhanced thorax computed tomography scan was performed to evaluate the relationship between the major mediastinal vascular structures and the mass. A left anterolateral thoracotomy was performed. The pathology was reported as an arterio-veno-lymphatic vascular malformation. Mediastinal LVMs are extremely rare but may present with severe life-threatening symptoms due to compression of major mediastinal structures. This report highlights that mediastinal LVM has a differential diagnosis and its management can be challenging.