Kawasaki disease in two cousins with atypical presentation: Case report
Turkiye Klinikleri Pediatri, cilt.19, sa.4, ss.347-349, 2010 (Scopus)
- Yayın Türü: Makale / Tam Makale
- Cilt numarası: 19 Sayı: 4
- Basım Tarihi: 2010
- Dergi Adı: Turkiye Klinikleri Pediatri
- Derginin Tarandığı İndeksler: Scopus
- Sayfa Sayıları: ss.347-349
- Anahtar Kelimeler: Lymphohistiocytosis, hemophagocytic, Mucocutaneous lymph node syndrome, Vasculitis
- Sağlık Bilimleri Üniversitesi Adresli: Hayır
Özet
Etiology of Kawasaki disease could not be fully understood, it is believed that there is a genetic susceptibility related to a number of genetic associations; and familial cases have been reported. Hereby we present a 7 year-old boy who had high fever, lymphadenopathy, rash, low acute phase reactants due to secondary hemophagocytosis. He also had a cousin who developed Kawasaki disease 10 years ago w i th a similar presentation who was eventually diagnosed as having Kawasaki Disease. This is the first familial case presented from Turkish population which reminds us that genetic susceptibility does exist in pathogenesis of Kawasaki disease. Copyright © 2009 by Tür kiye Klinikleri.