Mayer-rokitansky-kuster-hauser syndrome with presacral schwannoma presenting as a pelvic mass: A literature review and case report Pelvik kitle olarak prezente olan presakral schwannomlu mayer-rokitansky-küster-hauser sendromu ve literatürün gözden geçirilmesi


NARİN R., Özyazıcı S., NARİN M. A., Seyfettinoglu S., Aşut E.

Turkish Journal of Obstetrics and Gynecology, cilt.18, sa.4, ss.333-336, 2021 (ESCI, Scopus, TRDizin)

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 18 Sayı: 4
  • Basım Tarihi: 2021
  • Doi Numarası: 10.4274/tjod.galenos.2021.84032
  • Dergi Adı: Turkish Journal of Obstetrics and Gynecology
  • Derginin Tarandığı İndeksler: Emerging Sources Citation Index (ESCI), Scopus, TR DİZİN (ULAKBİM)
  • Sayfa Sayıları: ss.333-336
  • Anahtar Kelimeler: MRKH syndrome, schwannoma, pelvic mass
  • Sağlık Bilimleri Üniversitesi Adresli: Evet

Özet

A 32-year-old woman was admitted to our gynecology outpatient clinic with primary amenorrhea, a pelvic mass, and pain. Sonographic examination and magnetic resonance imaging revealed an approximately 124×103 mm heterogeneous mass. Moreover, laparotomy revealed fibrotic uterine bands with normal ovaries, tubes, and a solid retroperitoneal lesion. On the second postoperative day, the mass was removed, and the patient was discharged with full recovery. Microscopic examination of the pelvic mass confirmed the diagnosis of schwannoma. To the best of our knowledge, this is the first report on the co-occurrence of Mayer-Rokitansky-Küster-Hauser syndrome and schwannoma, without the presence of any other pathology.