Monomelic amyotrophy involving lower extremity: Case report Alt ekstremiteyi tutan monomelik amyotrofi: Olgu sunumu
Journal of Rheumatology and Medical Rehabilitation, cilt.19, sa.4, ss.196-199, 2008 (Scopus)
- Yayın Türü: Makale / Tam Makale
- Cilt numarası: 19 Sayı: 4
- Basım Tarihi: 2008
- Dergi Adı: Journal of Rheumatology and Medical Rehabilitation
- Derginin Tarandığı İndeksler: Scopus
- Sayfa Sayıları: ss.196-199
- Anahtar Kelimeler: Diabetic neuropathies, Electrodiagnosis, Lower extremity
- Sağlık Bilimleri Üniversitesi Adresli: Evet
Özet
Monomelic amyotrophy (MA) is a rare, benign motor neuron disorder. The disease is seen more frequent in men in the 2nd and 3rd decades. It is characterized by weakness and wasting limited to a single limb especially upper limb involvement. Legs are involved rarely and pyramidal findings are uncommon. The symptoms progress insidiously for 2-5 years followed by a spontaneous arrest. Electrophysiologic studies demonstrate reduced compound muscle action potential amplitudes in affected muscles. Needle electromyography (EMG) shows abnormal spontaneous activity at rest and also large amplitude motor unit potentials (MUP). We report a case of 42-years-old man who presented slowly progressive amyotrophy and distal paresis of the right lower limb, which was clinically stabilized within 4 years. We thought that monomelic amyotrophy should be kept in mind in differential diagnosis of patients presenting with amyotrophy involving a single lower or upper extremity. Copyright © 2008 by Türk Tibbi Rehabilitasyon Kurumu Derneǧi.