Brachial Amyotrophic Diplegia: Case Report Brakiyal amyotrofik dipleji: Olgu sunumu
Journal of Neurological Sciences, cilt.28, sa.1, ss.86-90, 2011 (SCI-Expanded, Scopus, TRDizin)
- Yayın Türü: Makale / Tam Makale
- Cilt numarası: 28 Sayı: 1
- Basım Tarihi: 2011
- Dergi Adı: Journal of Neurological Sciences
- Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus, TR DİZİN (ULAKBİM)
- Sayfa Sayıları: ss.86-90
- Anahtar Kelimeler: Brachial amyotrophic diplegia, Flail arm syndrome, Neurogenic man-in-a-barrel syndrome
- Sağlık Bilimleri Üniversitesi Adresli: Hayır
Özet
Two forms of Amyotrophic lateral sclerosis (ALS) subtypes have been recognized since the late 19th and early 20th centuries but relatively inadequately studied, these being the flail arm (FA) and flail leg (FL) syndromes. The FA phenotype was described by Vulpian in 1886 as a syndrome of proximal weakness and wasting of the upper limbs (scapulohumeral variant ofprogressive muscular atrophy or forme scapulo-humeérale). The condition has been variously termed as Vulpian-Bernhardt syndrome, hanging-arm syndrome, neurogenic man-in-a-barrel syndrome, brachial amyotrophic diplegia, or the FA syndrome. The syndrome typicallypresents with progressive upper limb weakness and wasting that is often symmetric andproximal, without significant functional involvement of lower limbs or bulbar muscles. Here we presented a patient with complaints of difficulty in lifting his right arm in his medical history. Brachial amyotrophic diplegia was diagnosed with neurological examination and EMG findings. It is presented because of rarity.