Prenatal diagnosis of right aortic arch: associated anomalies and fetal prognosis according to different subtypes


Dizdaroǧullarl G. E., Alplnar A., Demirci O.

Journal of Perinatal Medicine, cilt.52, sa.3, ss.304-309, 2024 (SCI-Expanded, Scopus)

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 52 Sayı: 3
  • Basım Tarihi: 2024
  • Doi Numarası: 10.1515/jpm-2023-0410
  • Dergi Adı: Journal of Perinatal Medicine
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.304-309
  • Anahtar Kelimeler: righ aortic arch, double aortic arch, fetal heart, prenatal diagnosis
  • Sağlık Bilimleri Üniversitesi Adresli: Evet

Özet

Objectives: Right aortic arch (RAA) is a rare anomaly with an incidence of 0.1% in the adult population and low-risk fetuses. Our aim in this study was to evaluate associated anomalies and conditions according to subtypes. Methods: This was a retrospective study examining consecutive pregnancies diagnosed with RAA in our hospital between 2018 and 2022. Fetuses with RAA were divided into three groups, RAA with right-sided ductus arteriosus (RAA-RDA), RAA with left-sided ductus arteriosus (RAA-LDA), and RAA with a double aortic arch (RAA-DAA). Results: A total of 81 fetuses were diagnosed as having RAA during the study period. The rate of cardiac anomalies (82.8%) in the RAA-RDA group was higher than in the RAA-LDA (17.6%) and RAA-DAA (22.2%) groups (p<0.001). No statistically significant difference was found between the groups in terms of maternal age, diagnosis week, pregnancy outcome, extracardiac anomalies, and genetic anomalies. Three (8%) of 36 fetuses with isolated RAA who resulted in live birth developed symptoms related to the vascular ring, and one (2.7%) newborn with RAA-DAA underwent surgery. Conclusions: The incidence of cardiac anomalies is high in fetuses with RAA-RDA. Ultrasound examinations should be performed for cardiac anomalies and additional structural anomalies. Vascular ring formation is a rare but important complication due to compression risk to the trachea and esophagus.