Case report: Scleroderma renal crisis presenting as thrombotic microangiopathy Olgu sunumu: Trombotik mikroanjiopati ile basvuran skleroderma renal kriz


Uǧur M. C., EKİNCİ F., Karadeniz T., Gram E., BAHADIR H., CEYLAN C., ...Daha Fazla

Turkish Nephrology, Dialysis and Transplantation Journal, cilt.25, ss.71-74, 2016 (Scopus, TRDizin)

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 25
  • Basım Tarihi: 2016
  • Doi Numarası: 10.5262/tndt.2016.12
  • Dergi Adı: Turkish Nephrology, Dialysis and Transplantation Journal
  • Derginin Tarandığı İndeksler: Scopus, TR DİZİN (ULAKBİM)
  • Sayfa Sayıları: ss.71-74
  • Anahtar Kelimeler: Scleroderma, Renal crisis, Thrombotic microangiopathy, Hemodialysis
  • Sağlık Bilimleri Üniversitesi Adresli: Evet

Özet

Scleroderma is a systemic autoimmune disease of unknown origin characterized by excessive deposition of collagen and other connective tissue macromolecules in multiple organs. It can cause thrombotic microangiopathy. Scleroderma renal crisis is a major complication of this disorder. We aimed to present a case that presented with thrombotic microangiopathy findings and was diagnosed as scleroderma renal crisis. A 56-year-old female patient presented with hypertension and thrombotic microangiopathy signs. After examination and renal biopsy, scleroderma renal crisis with thrombotic microangiopathy was diagnosed. A routine hemodialysis program and an angiotensin converting enzyme inhibitor was started Scleroderma renal crisis should be kept in mind in patients presenting with malignant hypertension and thrombotic microangiopathy.