A rare case of midaortic syndrome: Vascular Behçet’s disease or Takayasu arteritis?
Turkish Journal of Thoracic and Cardiovascular Surgery, cilt.34, sa.2, ss.172-174, 2026 (SCI-Expanded, Scopus)
- Yayın Türü: Makale / Tam Makale
- Cilt numarası: 34 Sayı: 2
- Basım Tarihi: 2026
- Doi Numarası: 10.4274/tjtcs.2025.27274
- Dergi Adı: Turkish Journal of Thoracic and Cardiovascular Surgery
- Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
- Sayfa Sayıları: ss.172-174
- Anahtar Kelimeler: Midaortic syndrome, Beh & ccedil;et's disease, Takayasu arteritis, resistant hypertension, aortitis
- Sağlık Bilimleri Üniversitesi Adresli: Evet
Özet
This case report describes a 44-year-old man with midaortic syndrome and resistant hypertension, presenting a diagnostic challenge due to overlapping features of Behçet’s disease and Takayasu arteritis. Imaging studies revealed severe aortic stenosis accompanied by aortic wall thickening, findings typically associated with Takayasu arteritis; however, the patient’s clinical history and a positive pathergy test supported a diagnosis of Behçet’s disease. Immunosuppressive therapy led to symptomatic improvement, and surgical management with thoracic endovascular aortic repair was successfully performed to address the aortic stenosis. This report discusses the possibility of Behçet’s disease presenting with aortic stenosis—a rare vascular complication—or the coexistence of Behçet’s disease and Takayasu arteritis.