Persistent craniopharyngeal canal, bilateral microphthalmia with colobomatous cysts, ectopic adenohypophysis with Rathke cleft cyst, and ectopic neurohypophysis: Case report and review of the literature


Akyel N. G., Alımlı A. G., Demirkan T. H., Sivri M.

Child's Nervous System, cilt.34, sa.7, ss.1407-1410, 2018 (SCI-Expanded, Scopus)

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 34 Sayı: 7
  • Basım Tarihi: 2018
  • Doi Numarası: 10.1007/s00381-018-3747-4
  • Dergi Adı: Child's Nervous System
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.1407-1410
  • Anahtar Kelimeler: Craniopharyngeal canal, Colobomatous cyst, Ectopic neurohypophysis, Rathke cleft, Cyst, Microphtalmos with cyst
  • Sağlık Bilimleri Üniversitesi Adresli: Evet

Özet

Introduction Persistent craniopharyngeal canal (PCC) is a rare anomaly of the base of the skull. PCC is defined as a wellcorticated osseous canal, extending from the roof of the nasopharynx to the base of the sella over the course of the sphenoid corpus. We reported a PCC case with unique associations. The magnetic resonance imaging findings are discussed. Case presentation We report a case of a 2-year-old boy with persistent craniopharyngeal canal, bilateral microphtalmia with large colobomatous cyst, and ectopic adenohypophysis with Rathke cleft cyst. He also has ectopic neurohypophysis and optic atrophy. Conclusion The presence of orbital and optic tract malformations, craniofacial and intracranial anomalies, and tumors can accompany craniopharyngeal canals (CCs). MRI is helpful in the evaluation of PCC and associated anomalies in these patients.