Giant Metastatic Intracardiac Malignant Fibrous Tumor Presenting with Supraventricular Tachycardia: A Case Report Supraventriküler Taşikardi ile Prezante Olan Dev Metastatik İntrakardiyak Malign Fibröz Tümör: Olgu Raporu
Turk Kardiyoloji Dernegi Arsivi, cilt.52, sa.8, ss.611-614, 2024 (ESCI, Scopus, TRDizin)
- Yayın Türü: Makale / Tam Makale
- Cilt numarası: 52 Sayı: 8
- Basım Tarihi: 2024
- Doi Numarası: 10.5543/tkda.2023.19310
- Dergi Adı: Turk Kardiyoloji Dernegi Arsivi
- Derginin Tarandığı İndeksler: Emerging Sources Citation Index (ESCI), Scopus, TR DİZİN (ULAKBİM)
- Sayfa Sayıları: ss.611-614
- Anahtar Kelimeler: Cardiac mass, cardio-oncology, solitary fibrous tumor
- Sağlık Bilimleri Üniversitesi Adresli: Evet
Özet
Solitary fibrous tumors (SFTs) are rare neoplasms originating from fibroblastic mesenchymal cells. This case report details a 43-year-old female patient with cardiac SFT, a rarity in the medical literature, who presented with palpitations and a known malignancy. Supraventricular tachycardia was diagnosed in the emergency department, and a subsequent echocardiography revealed a giant mass in the left atrium after sinus rhythm restoration. The mass, causing symptomatic severe mitral stenosis, necessitated surgical intervention. Pathological examination of the surgical specimens confirmed the diagnosis of SFT. Cardiac masses are extremely rare in clinical practice, and the literature on SFTs is primarily limited to case reports. More research is needed due to the scarcity of information on managing this condition.