Hemophagocytic Lymphohistiocytosis Associated With Hemolytic Uremic Syndrome in a Child: A Case Report and Systematic Literature Review


Tas N., Gokceoglu A. U., Yayla B. C., Ozcan A., SAÇ R., VEZİR E., ...Daha Fazla

Journal of Pediatric Hematology/Oncology, cilt.44, sa.5, 2022 (SCI-Expanded, Scopus)

  • Yayın Türü: Makale / Derleme
  • Cilt numarası: 44 Sayı: 5
  • Basım Tarihi: 2022
  • Doi Numarası: 10.1097/mph.0000000000002265
  • Dergi Adı: Journal of Pediatric Hematology/Oncology
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus, CAB Abstracts, EMBASE, MEDLINE
  • Anahtar Kelimeler: hemolytic-uremic syndrome, lymphohistiocytosis, hemophagocytic, anemia, hemolytic, hepatomegaly, splenomegaly
  • Sağlık Bilimleri Üniversitesi Adresli: Evet

Özet

Hemophagocytic lymphohistiocytosis (HLH) is a life-threatening disorder resulting from excessive activation and nonmalignant proliferation of T-lymphocytes and macrophages. Hemolytic uremic syndrome (HUS) is a disease characterized by microangiopathic hemolytic anemia, thrombocytopenia, and acute renal failure. Reports pertaining to the association between HLH and HUS are rarely published; however, we report on a 4-year-old boy who was diagnosed with both conditions and treated successfully with high-dose steroid and intravenous immunoglobulin. Differentiating HUS from HLH can be challenging because of their clinical similarities. Therefore, prompt diagnosis and immunosuppressive treatment are essential and life-saving to these patients.