Dilated cardiomyopathy in a patient with Marfan syndrome accompanied by chronic type A aortic dissection and right atrial thrombus
Internal Medicine, cilt.49, sa.23, ss.2583-2586, 2010 (SCI-Expanded, Scopus)
- Yayın Türü: Makale / Tam Makale
- Cilt numarası: 49 Sayı: 23
- Basım Tarihi: 2010
- Doi Numarası: 10.2169/internalmedicine.49.3880
- Dergi Adı: Internal Medicine
- Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
- Sayfa Sayıları: ss.2583-2586
- Anahtar Kelimeler: Marfan syndrome, dilated cardiomyopathy, aortic dissection
- Sağlık Bilimleri Üniversitesi Adresli: Evet
Özet
Marfan's syndrome (MFS) is an autosomal dominant disorder of connective tissue involving musculoskeletal, cardiovascular and ocular systems. Aortic disease is the leading cause of mortality in MFS. Among all, dilated cardiomyopathy in the absence of severe valvular dysfunction is a very rare cardiovascular feature of MFS. We report a case of biventricular heart failure in a patient with MFS, complicated by chronic type A aortic dissection and right atrial thrombus. This report clearly highlights the importance of close cardiovascular follow-up in patients with MFS. © 2010 The Japanese Society of Internal Medicine.