Pediatric Bentall procedure for giant ascending aortic aneurysm in Loeys-Dietz syndrome
Annals of Pediatric Cardiology, cilt.16, sa.3, ss.223-225, 2023 (ESCI, Scopus)
- Yayın Türü: Makale / Tam Makale
- Cilt numarası: 16 Sayı: 3
- Basım Tarihi: 2023
- Doi Numarası: 10.4103/apc.apc_22_23
- Dergi Adı: Annals of Pediatric Cardiology
- Derginin Tarandığı İndeksler: Emerging Sources Citation Index (ESCI), Scopus, Academic Search Premier, CINAHL, EMBASE, Directory of Open Access Journals
- Sayfa Sayıları: ss.223-225
- Anahtar Kelimeler: Aortic aneurysm, Bentall procedure, Loeys-Dietz syndrome
- Sağlık Bilimleri Üniversitesi Adresli: Evet
Özet
Ascending aortic aneurysm is very rare in children, and is usually seen in patients with underlying connective tissue disorders such as Marfans and Ehler-Danlos syndrome. Loeys-Dietz syndrome (LDS) is less commonly seen as a cause of ascending aortic aneurysms in children. In this case report, we describe pediatric Bentall procedure, which we successfully performed to a child with LDS (Type I) with giant ascending aortic enlargement and significant aortic regurgitation.