TAR syndrome with annular pancreas and anal atresia - A case report
European Journal of Pediatric Surgery, cilt.14, sa.2, ss.123-125, 2004 (Scopus)
- Yayın Türü: Makale / Tam Makale
- Cilt numarası: 14 Sayı: 2
- Basım Tarihi: 2004
- Doi Numarası: 10.1055/s-2004-815860
- Dergi Adı: European Journal of Pediatric Surgery
- Derginin Tarandığı İndeksler: Scopus
- Sayfa Sayıları: ss.123-125
- Anahtar Kelimeler: syndrome, anal atresia, annular pancreas
- Sağlık Bilimleri Üniversitesi Adresli: Evet
Özet
TAR syndrome is manifested by the presence of hypomegakaryocytic thrombocytopenia and the bilateral absence of radii. An 8-day-old female newborn was referred to our clinic with diagnosis of TAR syndrome and symptoms of intestinal obstruction. On perineal examination she also had anal atresia with rectovestibular fistula. Because of persistent bile-stained drainage from the nasogastric tube, an upper gastrointestinal contrast study was performed and partial duodenal obstruction was detected. At operation, an annular pancreas was encountered and side-to-side duodenoduodenostomy was performed. A small number of gastrointestinal system malformations associated with TAR syndrome has been reported. Our case is unique; the association with annular pancreas and anal atresia with rectovestibular fistula has never been previously reported.