Anaesthesia in Naxos disease: First case report
Bosnian Journal of Basic Medical Sciences, cilt.13, sa.1, ss.63-65, 2013 (SCI-Expanded, Scopus)
- Yayın Türü: Makale / Tam Makale
- Cilt numarası: 13 Sayı: 1
- Basım Tarihi: 2013
- Doi Numarası: 10.17305/bjbms.2013.2421
- Dergi Adı: Bosnian Journal of Basic Medical Sciences
- Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
- Sayfa Sayıları: ss.63-65
- Anahtar Kelimeler: Anaesthesia, Congestive heart failure, Intracardiac mural thrombus, Naxos disease
- Sağlık Bilimleri Üniversitesi Adresli: Evet
Özet
Naxos disease is a recessively inherited arrhythmogenic right ventricular cardiomyopathy in which the cardiac phenotype is associated with palmoplantar keratoderma and woolly hair. The hair phenotype is unique, characterized by congenital woolly, curly, rough, and light-colored scalp hair and sparse eyebrows. However, arrhythmias and severe cardiomyopathies are causes of severe life threatened intracardiac thrombus. Thrombus therapy needs private care and sedative, operative processes need to give close attention to these patients. In this case report, sedation given a patient who having severe congestive heart failure with huge mural thrombus in left ventriculus has been presented. © 2013 Association of Basic Medical Sciences of FBIH. All rights reserved.