Pulmonary Langerhans Cell Histiocytosis and Pulmonary Lymphangioleiomyomatosis
Airway Diseases: Volume 1-3, Springer International Publishing Ag, ss.1839-1860, 2023
- Yayın Türü: Kitapta Bölüm / Araştırma Kitabı
- Basım Tarihi: 2023
- Doi Numarası: 10.1007/978-3-031-22483-6_94-1
- Yayınevi: Springer International Publishing Ag
- Sayfa Sayıları: ss.1839-1860
- Sağlık Bilimleri Üniversitesi Adresli: Evet
Özet
Langerhans cell histiocytosis (LCH) encompasses the most common group of histiocytic disorders characterized by abnormal function and differentiation or proliferation of mononuclear phagocyte system cells, with a wide variety of clinical pictures and consequences [1]. It is caused by the disorder of myeloid dendritic cells and is thought to be an inflammatory myeloid neoplasm [2]. Histiocytes including Langerhans cells, monocytes/macrophages, dermal/interstitial dendritic cells are large white blood cells. Langerhans cell is normally found in the dermis, reticuloendothelial system, lung, and pleura [3, 4].