Usher syndrome associated with a variant of Dandy-Walker malformation.


ŞİMŞEK T., ÖZDAMAR EROL Y., Simsek E., TÜRE G.

Journal of pediatric ophthalmology and strabismus, cilt.47 Online, 2010 (SCI-Expanded, Scopus)

Özet

Three cases of Usher syndrome associated with a variant of Dandy-Walker malformation in three siblings from consanguineous Turkish parents are described. The siblings had retinitis pigmentosa and hearing loss. Two of the siblings also had mental retardation, which is not a constant finding in Usher syndrome. Dandy-Walker malformation might have contributed to the mental retardation in two of these patients and might be a coincidental finding with Usher syndrome. Copyright 2010, SLACK Incorporated.