Difficult Intubation and General Anesthesia Management in a Pediatric Patient with Xeroderma Pigmentosum Requiring Emergency Laparotomy Acil Laparotomi Gereken Xeroderma Pigmentosumlu Pediatrik Hastada Zor Entübasyon ve Genel Anestezi Yönetimi
Anestezi Dergisi, cilt.30, sa.2, ss.134-138, 2022 (Scopus, TRDizin)
- Yayın Türü: Makale / Tam Makale
- Cilt numarası: 30 Sayı: 2
- Basım Tarihi: 2022
- Doi Numarası: 10.54875/jarss.2022.30092
- Dergi Adı: Anestezi Dergisi
- Derginin Tarandığı İndeksler: Scopus, Academic Search Premier, Central & Eastern European Academic Source (CEEAS), EMBASE, TR DİZİN (ULAKBİM)
- Sayfa Sayıları: ss.134-138
- Anahtar Kelimeler: airway management, laryngoscopy, sevoflurane, sugammadex, Xeroderma pigmentosum
- Sağlık Bilimleri Üniversitesi Adresli: Evet
Özet
Xeroderma pigmentosum (XP) is one of the rare neurocutaneous syndromes. The lesions occurring due to an impairment in the DNA repair mechanisms caused by ultraviolet light often require surgical interventions. There is no standardized general anesthesia procedure to be used in these patients. Besides, it is not clear whether sevoflurane leads to deterioration in the neurological condition. There are also other problems that may be encountered during difficult intubation and extubation. This may be the first reported pediatric patient with XP that underwent emergency laparotomy under general anesthesia with the successful use of sevoflurane, videolaryngoscopy, and sugammadex.