ANCA associated vasculitis and related pulmonary alveolar hemorrhage in a patient with pulmonary alveolar proteinosis
Clinica Terapeutica, cilt.172, sa.5, ss.389-391, 2021 (Scopus)
- Yayın Türü: Makale / Tam Makale
- Cilt numarası: 172 Sayı: 5
- Basım Tarihi: 2021
- Doi Numarası: 10.7417/ct.2021.2344
- Dergi Adı: Clinica Terapeutica
- Derginin Tarandığı İndeksler: Scopus, EMBASE, MEDLINE
- Sayfa Sayıları: ss.389-391
- Anahtar Kelimeler: Alveolar hemorrhage, Lung, Pulmonary alveolar proteinosis, Vasculitis
- Sağlık Bilimleri Üniversitesi Adresli: Evet
Özet
Pulmonary Alveolar Proteinosis (PAP) is a rare lung disease characterized by accumulation of a lipoproteinous material in the alveoli and distal airways. Antibodies against granulocyte macrophage colony stimulant factor (GM-CSF) are thought to be responsible for its pathogenesis. Antineutrophilic cytoplasmic antibody (ANCA) associated vasculitis (AAV) is a group of vasculitis affecting small and medium vessels and often characterized by lung and kidney involvement. Here, we present a patient with PAP diagnosis who has been in remission for many years, developing AAV and associated pulmonary alveolar hemorrhage.