A new syndrome associated with absence of lower lid lacrimal punctum, ptosis, elevation deficiency of both eyes and mild facial dysmorphism


GÜRAN Ş., TORUN D., MUTLU F. M., UYSAL Y., Ugurel M. S., Bahce M.

Ophthalmic Genetics, cilt.30, sa.3, ss.146-151, 2009 (SCI-Expanded, Scopus)

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 30 Sayı: 3
  • Basım Tarihi: 2009
  • Doi Numarası: 10.1080/13816810902988772
  • Dergi Adı: Ophthalmic Genetics
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.146-151
  • Anahtar Kelimeler: Absence of lacrimal punctum, upper ocular movement limitation, ptosis, facial dysmorphism
  • Sağlık Bilimleri Üniversitesi Adresli: Evet

Özet

A considerable volume of literature has been published on the association of lacrimal outflow dysgenesis with developmental anomalies or systemic syndromes. We report three affected individuals in a consanguineous family those are associated with bilateral ptosis, upper ocular movement limitation, and absence of the lacrimal punctum. T our knowledge, this is the first article reporting the association of bilateral ptosis, facial dysmorphism, upper ocular movement limitation, and absence of the lacrimal punctum in a hereditary form. As a sole example, these findings may be accepted as a new syndrome with autosomal recessive pattern because of consanguinity.