Pediatric Nasal Lipoma with İntracranial Lipoma-Rare Case of Pai Syndrome
Indian Journal of Otolaryngology and Head and Neck Surgery, cilt.78, sa.3, ss.1773-1775, 2026 (ESCI, Scopus)
- Yayın Türü: Makale / Tam Makale
- Cilt numarası: 78 Sayı: 3
- Basım Tarihi: 2026
- Doi Numarası: 10.1007/s12070-025-06285-8
- Dergi Adı: Indian Journal of Otolaryngology and Head and Neck Surgery
- Derginin Tarandığı İndeksler: Emerging Sources Citation Index (ESCI), Scopus, Academic Search Ultimate (EBSCO), Health Research Premium Collection (ProQuest)
- Sayfa Sayıları: ss.1773-1775
- Anahtar Kelimeler: Intracranial lipoma, Nasal lipoma, Pai syndrome
- Sağlık Bilimleri Üniversitesi Adresli: Evet
Özet
Pai syndrome, first described in 1987, is characterized by the presence of a congenital nasal lipoma, a median cleft of the upper lip, nasal polyps, and an intracranial lipoma. A 7-year-old male patient presented to our clinic with a chief complaint of nasal obstruction. Imaging studies revealed an intracranial lipoma. Total excision of the nasal mass was performed, and histopathological examination confirmed it as a nasal lipoma. Given that the intracranial lipoma was symptomatic, follow-up was planned. Investigations for a preliminary diagnosis of Pai syndrome did not reveal other findings consistent with this syndrome. As the patient’s relatives declined genetic testing, the patient was closely monitored. In pediatric patients presenting with nasal masses, the presence of an intracranial mass must be ruled out with cranial imaging prior to surgical intervention. When Pai syndrome is suspected, the patient should undergo a multidisciplinary evaluation.