Our cases with Scimitar syndrome
Turkiye Klinikleri Cardiovascular Sciences, cilt.24, sa.1, ss.88-91, 2012 (Scopus)
- Yayın Türü: Makale / Tam Makale
- Cilt numarası: 24 Sayı: 1
- Basım Tarihi: 2012
- Dergi Adı: Turkiye Klinikleri Cardiovascular Sciences
- Derginin Tarandığı İndeksler: Scopus
- Sayfa Sayıları: ss.88-91
- Anahtar Kelimeler: Child, Congenital, Heart defects, Scimitar syndrome
- Sağlık Bilimleri Üniversitesi Adresli: Evet
Özet
Scimitar syndrome is a rare congenital cardiopulmonary system abnormality with an incidence of 0.001-0.003% that is characterized mostly with anomalous pulmonary venous drainage from right lung to the inferior vena cava instead of the left atrium, hypoplasia of the right lung and right pulmonary artery with dextroposition of the heart, and anomalous systemic arterial blood supply to the right lung. There also may be anomalies of the bronchial supply to the right lung; therefore, sequestration is frequently present. We present three cases with Scimitar syndrome, two of them were recognized while investigating for recurrent pulmonary infection and one of them was determined incidentally during catheterization. Two cases with recurrent pulmonary infection were researched for an opacity localized at the inferior zone of the right lung on the plain chest radiography. The other case was recognized during the angiographic study of descending aorta for aort coarctation when an abnormal artery supplying the inferior zone of the right lung was seen. Copyright © 2012 by Türkiye Klinikleri.