Argininosuccinic aciduria in a neonate presented with inspiratory stridor İnspiratuvar stridor klinik bulgusu ile saptanan argininosüksinik asidüri: Yenidoǧan olgusu


CAN E., BÜLBÜL A., Uslu S., Nuhoǧlu A.

Turk Pediatri Arsivi, cilt.46, sa.1, ss.84-86, 2011 (SCI-Expanded, Scopus, TRDizin)

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 46 Sayı: 1
  • Basım Tarihi: 2011
  • Doi Numarası: 10.4274/tpa.46.15
  • Dergi Adı: Turk Pediatri Arsivi
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus, TR DİZİN (ULAKBİM)
  • Sayfa Sayıları: ss.84-86
  • Anahtar Kelimeler: Argininosuccinic aciduria, inspiratory stridor, newborn
  • Sağlık Bilimleri Üniversitesi Adresli: Evet

Özet

A newborn, who was brought because of severe inspiratory stridor, was diagnosed argininosuccinic aciduria after laboratory tests. This case is presented because it is the first time of a patient to be presented with inspiratory stridor in argininosuccinic aciduria and to emphasize metabolic disease screening in newborns with inspiratory stridor without anatomic pathology.