A case of lipoid proteinosis with hippocampal calcification


Basekim C., Kizilkaya E., KUTLAY A. M., Karsli A.

Rivista di Neuroradiologia, cilt.8, sa.4, ss.589-591, 1995 (Scopus)

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 8 Sayı: 4
  • Basım Tarihi: 1995
  • Doi Numarası: 10.1177/197140099500800415
  • Dergi Adı: Rivista di Neuroradiologia
  • Derginin Tarandığı İndeksler: Scopus
  • Sayfa Sayıları: ss.589-591
  • Anahtar Kelimeler: LIPOID PROTEINOSIS, HIPPOCAMPAL CALCIFICATION
  • Sağlık Bilimleri Üniversitesi Adresli: Evet

Özet

Lipoid proteinosis is a rare autosomal recessive disorder. It primarily affects skin and mucosae, and is accepted as a systemic disorder. It is characterized by deposition of hyaline material in the arteriocapillary wall and epithelial membranes. This study describes a case of lipoid proteinosis with hippocampal calcification.