Rigid external maxillary distraction and rhinoplasty for pyknodysostosis


Varol A., Sabuncuoglu F. A., Sencimen M., Akcam T., Olmez H., Basa S.

Journal of Craniofacial Surgery, cilt.22, sa.3, ss.901-904, 2011 (SCI-Expanded, Scopus)

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 22 Sayı: 3
  • Basım Tarihi: 2011
  • Doi Numarası: 10.1097/scs.0b013e31820f7f3c
  • Dergi Adı: Journal of Craniofacial Surgery
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.901-904
  • Anahtar Kelimeler: Pyknodysostosis, RED II, midfacial hypoplasia
  • Sağlık Bilimleri Üniversitesi Adresli: Evet

Özet

AIM: This article reports the treatment of an 33-year-old female patient with pyknodysostosis by rigid external distraction II midface distraction system. Study Design: The patient with pyknodysostosis described in this report had severe midfacial hypoplasia. Correction of this by use of routine orthognathic surgery would require osteosynthesis and bone grafting. Risk of infection and/or nonunion after such a surgical procedure was considered too great, and therefore the possibility of treatment by distraction osteogenesis of the maxilla was evaluated. The rigid external distraction II midface distraction system was used to relocate the hypoplastic maxilla at anterior-inferior projection. Conclusions: Distraction osteogenesis should be considered as the primary reconstructive method for maxillofacial deformities in patients with sclerosing bone dysplasias, since this is the second reported case treated successfully with rigid external distraction. Copyright © 2011 by Mutaz B. Habal, MD.