CNS involvement of Langerhans cell histiocytosis. Report of 23 surgically treated cases


BELEN A. D., Çolak A., Özean O. E.

Neurosurgical Review, cilt.19, sa.4, ss.247-252, 1996 (Scopus)

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 19 Sayı: 4
  • Basım Tarihi: 1996
  • Doi Numarası: 10.1007/bf00314840
  • Dergi Adı: Neurosurgical Review
  • Derginin Tarandığı İndeksler: Scopus
  • Sayfa Sayıları: ss.247-252
  • Anahtar Kelimeler: brain, eosinophilic granuloma, Langerhans cell histiocytosis, spinal cord
  • Sağlık Bilimleri Üniversitesi Adresli: Evet

Özet

We present 23 cases of Langerhans cell histiocytosis with central nervous system (CNS) involvement. The major complaints were a mass on the cranial vault in fifteen (65%), visual disturbance in four (16%), polyurea-polydipsia in three (13%), and progressive weakness in all extremities in one patient (4%). Neurological examination revealed no abnormality in sixteen patients (70%), cranial nerve palsy, visual field defect and optic atrophy in six (26%) and paraparesis in one (4%). Tumoral mass was found to be located on the cranial vault (65%), in the suprasellar region (21%) and in the spinal column (8%). The cranium and spinal column were both involved in one patient. All patients underwent surgery; craniectomy with grossly total tumor excision plus cranioplasty (65%), craniotomy with subtotal tumor excision (26%), and vertebrectomy with grafting (13%) were performed. The clinical, radiological and histopathological features, as well as therapeutical considerations are discussed and the pertinent literature is reviewed.