Congenital lobar emphysema in an adult patient: Case report
Turkiye Klinikleri Journal of Medical Sciences, cilt.29, sa.6, ss.1780-1783, 2009 (SCI-Expanded, Scopus)
- Yayın Türü: Makale / Tam Makale
- Cilt numarası: 29 Sayı: 6
- Basım Tarihi: 2009
- Dergi Adı: Turkiye Klinikleri Journal of Medical Sciences
- Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
- Sayfa Sayıları: ss.1780-1783
- Anahtar Kelimeler: Congenital, emphyema, adult, surgery
- Sağlık Bilimleri Üniversitesi Adresli: Evet
Özet
Congenital lobar emphysema (CLE) is a rare bronchopulmonary malformation which may cause severe respiratory distress with symptoms such as cough, dyspnea, tachypnea, retraction of the chest, wheezing and cyanosis in the neonatal period. Several mechanisms of CLE have been proposed, including dysplastic or absent bronchial cartilage, endobronchial obstruction, extensive mucosal proliferation and infolding, extrinsic compression of the bronchi by the aberrant cardiopulmonary vasculature, and diffuse bronchial abnormalities. However, approximately half of these are due to unknown causes. Typical findings include overinflation of a pulmonary lobe with mediastinal shift to the contralateral side and compression in the adjacent parenchyma. Most children with CLE present symptoms before 6 months of age. Diagnosis of CLE in adulthood is unusual, and patients often present with mild symptoms. We discussed a case of CLE in an adult who diagnosed intraoperatively and treated with lobectomy. Copyright © 2009 by Türkiye Klinikleri.