Case report: POEMS syndrome in childhood
Journal of Pediatric Hematology/Oncology, cilt.30, sa.3, ss.235-238, 2008 (SCI-Expanded, Scopus)
- Yayın Türü: Makale / Tam Makale
- Cilt numarası: 30 Sayı: 3
- Basım Tarihi: 2008
- Doi Numarası: 10.1097/mph.0b013e31815f88da
- Dergi Adı: Journal of Pediatric Hematology/Oncology
- Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
- Sayfa Sayıları: ss.235-238
- Anahtar Kelimeler: pOEMS, polyneuropathy, organomegaly, endocrinopathy, gammopathy, children
- Sağlık Bilimleri Üniversitesi Adresli: Evet
Özet
POEMS syndrome is a rare multisystem disorder, which is characterized by polyneuropathy, organomegaly, endocrinopathy, monoclonal gammopathy, and skin changes. We report a 15-year-old girl with POEMS syndrome, who developed growth retardation, delayed puberty, gradually increasing abdominal distention, brown skin pigmentation, hypogonadism, hepatosplenomegaly, lympadenomegaly, monoclonal gammopathy, and anemia. The patient dramatically responded to pulse steroid therapy. To our knowledge, this patient is one of the youngest reported cases of POEMS syndrome. © 2008 Lippincott Williams & Wilkins, Inc.