Congenital bilateral perisylvian syndrome: A case report Konjenital bilateral perisilviyan sendrom: Olgu sunumu


VURUCU S., Afyoncu A. O., Kocaoǧlu M., Gül D., Akin R.

Gulhane Medical Journal, cilt.51, sa.1, ss.64-66, 2009 (Scopus, TRDizin)

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 51 Sayı: 1
  • Basım Tarihi: 2009
  • Dergi Adı: Gulhane Medical Journal
  • Derginin Tarandığı İndeksler: Scopus, TR DİZİN (ULAKBİM)
  • Sayfa Sayıları: ss.64-66
  • Anahtar Kelimeler: Congenital bilateral perisylvian syndrome, Epilepsy, Perisylvian cortical dysplasia, Pseudobulbar palsy
  • Sağlık Bilimleri Üniversitesi Adresli: Evet

Özet

Congenital bilateral perisylvian syndrome is a rare syndrome characterized with mental retardation, speech retardation, pseudobulbar palsy, epilepsy and bilateral neuronal migration defects in the perisylvian area on brain magnetic rezonans imaging. It may be due to genetic or non-genetic reasons. We herein report a case presenting with complex partial seizures, speech retardation, bilateral fascial diplegia and polymicrogyria findings on brain magnetic resonance imaging and diagnosed to have congenital bilateral perisylvian syndrome as it is very rare. © Gülhane Askeri Ti{dotless}p Akademisi 2009.