Right ventricular blood cyst in an adult autosomal dominant polycystic kidney disease patient: An unusual association


Simsek E. C., Oncel D., Ozel E.

Journal of the College of Physicians and Surgeons Pakistan, cilt.31, sa.12, ss.1500-1502, 2021 (SCI-Expanded, Scopus)

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 31 Sayı: 12
  • Basım Tarihi: 2021
  • Doi Numarası: 10.29271/jcpsp.2021.12.1500
  • Dergi Adı: Journal of the College of Physicians and Surgeons Pakistan
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus, CAB Abstracts, EMBASE, MEDLINE, Veterinary Science Database
  • Sayfa Sayıları: ss.1500-1502
  • Anahtar Kelimeler: Autosomal dominant polycystic kidney disease, Cardiac blood cyst, Extra-renal manifestations
  • Sağlık Bilimleri Üniversitesi Adresli: Evet

Özet

Blood cysts of the heart are unusual primary cardiac tumor-like masses, which are usually located on the cardiac valves. These are very rare in adults, especially in a non-valvular location. Autosomal-dominant polycystic kidney disease (ADPKD) typically presents with multiple bilateral renal cysts, resulting in chronic kidney disease. Whilst many of the extra-renal manifestations of ADPKD are well-documented, associated cardiac masses are extremely rare: And cardiac blood cyst has not been reported in a patient with APKD to date. We present a 57-year man with a history of ADPKD and end-stage renal disease with a 2-cm-diameter right ventricular blood cyst, which was detected on multimodality imaging.