Myocardial ventricular noncompaction: Recent literature due to its rarity in childhood Miyokardiyal Ventriküler Nonkompaksiyon: Çocuklukta Nadir Görülmesi Nedeniyle Son Literatürün Taranması
Guncel Pediatri, cilt.13, sa.2, ss.138-142, 2015 (Scopus)
- Yayın Türü: Makale / Tam Makale
- Cilt numarası: 13 Sayı: 2
- Basım Tarihi: 2015
- Doi Numarası: 10.4274/jcp.23753
- Dergi Adı: Guncel Pediatri
- Derginin Tarandığı İndeksler: Scopus
- Sayfa Sayıları: ss.138-142
- Anahtar Kelimeler: Ventricular myocardial noncompaction, childhood
- Sağlık Bilimleri Üniversitesi Adresli: Evet
Özet
Myocardial noncompaction is a rare form of congenital cardiomyopathy. The disorder represents an arrest of normal embryogenesis of myocardium in utero. It is characterized by deep trabecular structures anatomically and deep intratrabecular recesses. Congestive heart failure, thromboembolism and cardiac arrhythmias are main clinical findings. On the other hand patients may be asymptomatic. We describe a case of myocardial noncompaction presenting with decreased exercise capacity in our clinic. We would like to remind this rare disorder and search recent literatures.